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KMID : 1103720120670050367
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Journal of the Korean Society of Radiology
2012 Volume.67 No. 5 p.367 ~ p.370
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An Isolated Pulmonary Hematoma Mimicking a Lung Tumor as the Initial Finding of Vascular Ehlers-Danlos Syndrome
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Kang Eun-Ju
Lee Ki-Nam
Choi Pill-Jo
Ki Chang-Seok
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Abstract
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The vascular type of Ehlers-Danlos syndrome (vEDS) is an uncommon inherited disorder characterized by abnormalities in type III collagen, presenting itself as arterial dissection or rupture. We report a case of an isolated pulmonary hematoma mimicking a lung tumor in an 18-year-old man which turned out to be the initial finding of vEDS. Pneumothorax and hemothorax occurred repeatedly for 15 months following the surgical removal of the mass, and were treated by repeated left upper and lower lobectomy and thoracotomy. The diagnosis of vEDS was confirmed by pathologic and genetic studies.
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KEYWORD
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Ehlers-Danlos Syndrome, Lung, CT
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